General outline Another peculiar language disorder with
prominent impairment of meaning (words, objects, and faces) gradually progressing
Symptoms Starts with anomia, patients will ask for the
meaning of words or objects and may initially appear to have a hearing disorder.
Patients may develop routines for eating (compulsive).
Course Gradually progressive, after 5 years developing into FTD.
Age of onset: same as FTD; Average survival as FTD.
Caregiver problems Communication, and sometimes aloof, rigid, repetitive behaviours of patients.
Epidemiology: VERY RARE DISEASE
Aetiology Same as PPA (heterogeneous), depends on localisation.
The localisation of the degenerative process is left temporal .
DIAGNOSTIC PROCEDURES : Semantic impairment, hypoperfusion
of the temporal cortex, bilateral but with a left predominance