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Progressive primary aphasia
General
outline Language disorder - A peculiar disease
starting with progressive impairment of verbal skills developing
into fronto-temporal dementia after several years.
Synonyms Slowly Progressive Aphasia
Symptoms The key feature is impaired verbal fluency,
agrammatism, impaired comprehension of word scanning and naming deficit.
Despite their communication problems, patients at a mild stage are able to
continue usual activities of daily life and even may continue working.
Two forms: non-fluent and fluent forms of PPA.
After an average of 5 years and more, patients gradually develop clinical symptoms of FTD.
Course Gradually progressive language disorder, making
communication more and more difficult. After an average of 5 years or more
patients gradually develop the clinical symptoms of FTD with relative sparing
of memory. Average onset around 60, average survival time 6 - 8 years
Caregiver problems Communication
Epidemiology About 10% of fronto-temporal degeneration
Aetiology Pathologically PPA belongs to the family of
fronto-temporal degenerations and frequently abnormal tau is found. Localisation
?
Diagnostic procedures Same as FTD
Treatment and rehabilitation No specific medication.
Language rehabilitation has not been tried
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